Dental manifestations of hereditary hemorrhagic telangiectasia: a clinical case
نویسندگان
چکیده
A rare disorder that changes the blood vessels of many organs and causes bleeding. The disease affects lungs, liver, central nervous system, gastrointestinal tract, skin mucous membranes. degree incidence Randu-Weber-Osler is not high ranges from 1 detected case per 50 thousand – 100 population. scientific article presents a clinical with dental manifestations indicates important role dentist in monitoring such patients. red border lips dry, pale, pronounced multiple punctate telangiectasias red-violet color. In area lower lip, brightly colored round nodules diameter about 5 mm are found, protruding above surface, painless on palpation. On dorsal lateral surfaces, there papular formations color, to 7 mm, surface. gums hyperemic, edematous, loose, bleeds probing, periodontal pockets exudative contents. examination, attention was drawn an insufficient amount saliva, which located mainly retromolar region; it frothy. salivation rate reduced (0.1 ml minute). It assumed before during invasive procedures, antibiotic therapy necessary, especially when working infected areas (500 mg amoxicillin) every 8 hours starting 12 procedure for days. Given hypoxia cerebral embolism frequent complications, chair should be upright position throughout patient's appointment. Treatment this only supportive nature, its goals relieve symptoms, treat complications prevent progression disease. Early definition careful observation patient gives favorable prognosis course prevents development severe complications. Keywords: hereditary hemorrhagic telangiectasia, periodontitis, xerostomia.
منابع مشابه
Clinical manifestations of hereditary hemorrhagic telangiectasia.
Sixty-four patients with symptomatic hereditary hemorrhagic telangiectasia were retrospectively studied in order to determine the true incidence of clinical manifestations in this disease. This select group had a significantly higher incidence of gastrointestinal hemorrhage and pulmonary arteriovenous fistula formation than has been previously reported. Data are presented regarding the course a...
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Hereditary hemorrhagic telangiectasia, also known as Osler-Weber-Rendu disease, is an autosomal dominant disorder of the fibrovascular tissue. It is characterized by the classic triad of mucocutaneous telangiectasias, recurrent hemorrhages, and familial occurrence. The cutaneous manifestation appear clinically as punctuate, linear, or splinter-like telangiectasias of the upper body, oral, and n...
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BACKGROUND AND PURPOSE Patients with hereditary hemorrhagic telangiectasia (HHT) are at risk for developing cerebral vascular malformations and pulmonary arteriovenous fistulae. We assessed the risk of neurological dysfunction from these malformations and fistulae. METHODS Three hundred twenty-one consecutive patients with HHT seen at a single institution over a 20-year period were studied. A...
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ژورنال
عنوان ژورنال: ???????? ???????? ? ??????
سال: 2022
ISSN: ['2414-4495']
DOI: https://doi.org/10.35339/msz.2022.91.2.eny